Dehiscencia completa de tubo valvulado aórtico, evaluación y correlación entre eco doppler color y tomografía multislice cardíaca. Reporte de caso

Authors

DOI:

https://doi.org/10.37615/retic.v9n1a5

Keywords:

Marfan syndrome, aortic aneurysm, heart valve prosthesis, postoperative complications, case reports

Abstract

Aortic dilation is found in approximately 50-83 % of children with Marfan syndrome and progresses over time. Prophylactic aortic root repair has had the greatest impact on the survival of patients with MFS and a dilated aortic root. In its elective form, proximal aortic replacement has 30-day morbidity and mortality of 1.5 %. However, emergency replacement (within 24 h of consultation) is associated with increased 30-day mortality by 11.7 %. This underscores the importance of carefully timing elective surgical intervention to avoid the increased risk with emergency operations.

Downloads

Download data is not yet available.

Metrics

Metrics Loading ...

References

Faivre L, Masurel-Paulet A, Collod-Béroud G, et al. Clinical and molecular study of 320 children with Marfan syndrome and related type I fibrillinopathies in a series of 1009 probands with pathogenic FBN1 variants. Pediatrics. 2009;123(1):391-398. doi:10.1542/peds.2008-0703 DOI: https://doi.org/10.1542/peds.2008-0703

Pyeritz RE. Marfan syndrome: 30 years of research equals 30 years of additional life expectancy. Heart. 2009;95:173-175. doi:10.1136/hrt.2008.160515 DOI: https://doi.org/10.1136/hrt.2008.160515

Roman MJ, Rosen SE, Kramer-Fox R, et al. Prognostic significance of the pattern of aortic root dilation dilation in the Marfan syndrome. J Am Coll Cardiol. 1993;22:1470-1476. doi:10.1016/0735-1097(93)90559-J DOI: https://doi.org/10.1016/0735-1097(93)90559-J

Writing Committee Members, ACC/AHA Joint Committee on Clinical Practice Guidelines. 2022 ACC/AHA guideline for the diagnosis and management of aortic disease. Circulation. 2022;146:e334-e482. doi:10.1161/CIR.0000000000001106 DOI: https://doi.org/10.1161/CIR.0000000000001106

Carrel T, Berdat P, Pavlovic M, Sukhanov S, et al. Surgery of the dilated aortic root and ascending aorta in pediatric patients: techniques and results. Eur J Cardiothorac Surg. 2003;24:249-254. doi:10.1016/S1010-7940(03)00302-6 DOI: https://doi.org/10.1016/S1010-7940(03)00302-6

Habib G, Hoen B, Tornos P, et al. Guidelines on the prevention, diagnosis, and treatment of infective endocarditis (new version 2009). Eur Heart J. 2009;30:2369-2413. doi:10.1093/eurheartj/ehp285 DOI: https://doi.org/10.1093/eurheartj/ehp285

Wang A, Athan E, Pappas PA, et al. Contemporary clinical profile and outcome of prosthetic valve endocarditis. JAMA. 2007;297:1354-1361. doi:10.1001/jama.297.12.1354 DOI: https://doi.org/10.1001/jama.297.12.1354

Nagpal A, Sohail MR, Steckelberg JM. Prosthetic valve endocarditis: state of the heart. Clin Investig (Lond). 2012;2:803-817. doi:10.4155/CLI.12.70 DOI: https://doi.org/10.4155/cli.12.70

Published

2026-04-20

How to Cite

1.
Strada BN, Perello L. Dehiscencia completa de tubo valvulado aórtico, evaluación y correlación entre eco doppler color y tomografía multislice cardíaca. Reporte de caso. Rev Ecocardiogr Pract Otras Tec Imag Card (RETIC) [Internet]. 2026 Apr. 20 [cited 2026 Jun. 6];9(1):27-30. Available from: https://www.imagenretic.org/RevEcocarPract/article/view/731